Dravet syndrome is a rare type of lifelong epilepsy. The first signs of this syndrome are the occurrence of epileptic seizures during the first year of life in a normally developing infant.
The seizure types and frequency vary but usually persist throughout the patient’s lifetime. This syndrome also affects cognitive, motor and behavioural development.
Dravet syndrome has an age-dependent evolution. Three stages may be identified:
Psychomotor development is usually normal throughout the first year of life.
Based on the clinical experience of a number of expert physicians, early appropriate management of Dravet syndrome seems to result in a better outcome regarding long-term evolution and life expectancy in comparison to published data.